TopFIND 4.0

P50136: 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial

General Information

Protein names
- 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
- 1.2.4.4
- Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain
- BCKDE1A
- BCKDH E1-alpha
Gene names Bckdha
Organism Mus musculus
Protease Family
Protease ID
Chromosome location
UniProt ID P50136

1

N-termini

1

C-termini

0

Cleavages

0

Substrates

Sequence

        10         20         30         40         50         60 
MSAAKIWRPS RGLRQAALLL LGRSGVRGLA RSHPSRQQQQ QFPSLDDKPQ FPGASAEFVD 
        70         80         90        100        110        120 
KLEFIQPNVI SGIPIYRVMD RQGQIINPSE DPHLPQEEVL KFYRSMTLLN TMDRILYESQ 
       130        140        150        160        170        180 
REGRISFYMT NYGEEGTHVG SAAALERTDL VFGQYREAGV LMYRDYPLEL FMSQCYGNVN 
       190        200        210        220        230        240 
DPGKGRQMPV HYGCKERHFV TISSPLATQI PQAVGAAYAA KRANANRIVI CYFGEGAASE 
       250        260        270        280        290        300 
GDAHAGFNFA ATLECPIIFF CRNNGYAIST PTSEQYRGDG IAARGPGYGI KSIRVDGNDV 
       310        320        330        340        350        360 
FAVYNATKEA RRRAVAENQP FLIEAMTYRI GHHSTSDDSS AYRSVDEVNY WDKQDHPISR 
       370        380        390        400        410        420 
LRQYLLNQGW WDEEQEKAWR KQSRKKVMEA FEQAERKLKP NPSLLFSDVY QEMPAQLRRQ 
       430        440    
QESLARHLQT YGEHYPLDHF EK

Isoforms



Sequence View



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Protein Neighborhood

Domains & Features

1 N-termini - 1 C-termini - 0 Cleavages - 0 Substrates

N-termini

C-termini

    Name Sequence Position Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)
    ...DHFEK 442 inferred from electronic annotation electronic annotation UniProtKB inferred from uniprot

Cleavages

    Protease Position Sequence Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)

Substrates

    Substrate Position Sequence Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)