Q96RQ3: Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
Protein names | - Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial - MCCase subunit alpha - 6.4.1.4 - 3-methylcrotonyl-CoA carboxylase 1 - 3-methylcrotonyl-CoA carboxylase biotin-containing subunit - 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha |
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Gene names | MCCC1 |
Organism | Homo sapiens |
Protease Family | |
Protease ID | |
Chromosome location | |
UniProt ID | Q96RQ3 |
3
N-termini
3
C-termini
0
Cleavages
0
Substrates
Sequence
10 20 30 40 50 60
MAAASAVSVL LVAAERNRWH RLPSLLLPPR TWVWRQRTMK YTTATGRNIT KVLIANRGEI
70 80 90 100 110 120
ACRVMRTAKK LGVQTVAVYS EADRNSMHVD MADEAYSIGP APSQQSYLSM EKIIQVAKTS
130 140 150 160 170 180
AAQAIHPGCG FLSENMEFAE LCKQEGIIFI GPPPSAIRDM GIKSTSKSIM AAAGVPVVEG
190 200 210 220 230 240
YHGEDQSDQC LKEHARRIGY PVMIKAVRGG GGKGMRIVRS EQEFQEQLES ARREAKKSFN
250 260 270 280 290 300
DDAMLIEKFV DTPRHVEVQV FGDHHGNAVY LFERDCSVQR RHQKIIEEAP APGIKSEVRK
310 320 330 340 350 360
KLGEAAVRAA KAVNYVGAGT VEFIMDSKHN FCFMEMNTRL QVEHPVTEMI TGTDLVEWQL
370 380 390 400 410 420
RIAAGEKIPL SQEEITLQGH AFEARIYAED PSNNFMPVAG PLVHLSTPRA DPSTRIETGV
430 440 450 460 470 480
RQGDEVSVHY DPMIAKLVVW AADRQAALTK LRYSLRQYNI VGLHTNIDFL LNLSGHPEFE
490 500 510 520 530 540
AGNVHTDFIP QHHKQLLLSR KAAAKESLCQ AALGLILKEK AMTDTFTLQA HDQFSPFSSS
550 560 570 580 590 600
SGRRLNISYT RNMTLKDGKN NVAIAVTYNH DGSYSMQIED KTFQVLGNLY SEGDCTYLKC
610 620 630 640 650 660
SVNGVASKAK LIILENTIYL FSKEGSIEID IPVPKYLSSV SSQETQGGPL APMTGTIEKV
670 680 690 700 710 720
FVKAGDKVKA GDSLMVMIAM KMEHTIKSPK DGTVKKVFYR EGAQANRHTP LVEFEEEESD
KRESE
Isoforms
Sequence View
Protein Neighborhood
Domains & Features
3 N-termini - 3 C-termini - 0 Cleavages - 0 Substrates
N-termini
Name | Sequence | Position | Modification | Evidence type | Method | Source (database) | Source (Lab) | Evidence name | Publications (PMID) |
---|---|---|---|---|---|---|---|---|---|
Q96RQ3-42-unknown | TTATGR... | 42 | inferred from electronic annotation | electronic annotation | UniProtKB | inferred from uniprot | |||
Q96RQ3-110-unknown | MEKIIQ... | 110 | inferred from electronic annotation | unknown | Ensembl | inferred from ensembl protein ENSP00000419898 | |||
Q96RQ3-136-unknown | MEFAEL... | 136 | inferred from electronic annotation | unknown | Ensembl | inferred from ensembl protein ENSP00000441253 |
C-termini
Name | Sequence | Position | Evidence type | Method | Source (database) | Source (Lab) | Evidence name | Publications (PMIDs) |
---|---|---|---|---|---|---|---|---|
...DGKNNV | 561 | inferred from electronic annotation | unknown | Ensembl | inferred from ensembl protein ENSP00000441253 | |||
...SSQETQ | 645 | inferred from electronic annotation | unknown | Ensembl | inferred from ensembl protein ENSP00000420433 | |||
...KRESE | 725 | inferred from electronic annotation | electronic annotation | UniProtKB | inferred from uniprot |
Cleavages
Protease | Position | Sequence | Evidence type | Method | Source (database) | Source (Lab) | Evidence name | Publications (PMIDs) |
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Substrates
Substrate | Position | Sequence | Evidence type | Method | Source (database) | Source (Lab) | Evidence name | Publications (PMIDs) |
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