TopFIND 4.0

Q99LS1: Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial

General Information

Protein names
- Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial
- CblD {ECO:0000250|UniProtKB:Q9H3L0}

Gene names Mmadhc
Organism Mus musculus
Protease Family
Protease ID
Chromosome location
UniProt ID Q99LS1

1

N-termini

3

C-termini

0

Cleavages

0

Substrates

Sequence

        10         20         30         40         50         60 
MAHVLCNRAR LVSYLPGFCS LVKRVINPRA FSTAGSSGSD ESHVATAPPD ICSRTVWPDE 
        70         80         90        100        110        120 
TMGPFGPQDQ RFQLPGNIGF DCHLNGTASQ KKSQAHKTLP DVLAEPLSTE RHEFVMAQYV 
       130        140        150        160        170        180 
NEFQDSDAPV EQEINSAETY FESAKVECAI QTCPELLRRD FESLFPEVAN SKLMILTVTQ 
       190        200        210        220        230        240 
KTENDMTVWS EEVEVEREVL LEKFISGAKE ICYALRAEGY WADFIDPSSG VAFFGPYTNN 
       250        260        270        280        290    
TLFETDERYR HLGFSVDDLG CCKVIRHSLW GTHVVVGSIF TNATADSSIM RKLSGN

Isoforms



Sequence View



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(REFRESH)

Directness:


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Protease Assignment Confidence:


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Protein Neighborhood

Domains & Features

1 N-termini - 3 C-termini - 0 Cleavages - 0 Substrates

N-termini

    Name Sequence Position Modification Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMID)
    Q99LS1-39-unknown SDESHV... 39 inferred from electronic annotation electronic annotation UniProtKB inferred from uniprot

C-termini

Cleavages

    Protease Position Sequence Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)

Substrates

    Substrate Position Sequence Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)