TopFIND 4.0

P00480: Ornithine carbamoyltransferase, mitochondrial

General Information

Protein names
- Ornithine carbamoyltransferase, mitochondrial
- 2.1.3.3
- Ornithine transcarbamylase
- OTCase

Gene names OTC
Organism Homo sapiens
Protease Family
Protease ID
Chromosome location
UniProt ID P00480

2

N-termini

2

C-termini

1

Cleavages

0

Substrates

Sequence

        10         20         30         40         50         60 
MLFNLRILLN NAAFRNGHNF MVRNFRCGQP LQNKVQLKGR DLLTLKNFTG EEIKYMLWLS 
        70         80         90        100        110        120 
ADLKFRIKQK GEYLPLLQGK SLGMIFEKRS TRTRLSTETG FALLGGHPCF LTTQDIHLGV 
       130        140        150        160        170        180 
NESLTDTARV LSSMADAVLA RVYKQSDLDT LAKEASIPII NGLSDLYHPI QILADYLTLQ 
       190        200        210        220        230        240 
EHYSSLKGLT LSWIGDGNNI LHSIMMSAAK FGMHLQAATP KGYEPDASVT KLAEQYAKEN 
       250        260        270        280        290        300 
GTKLLLTNDP LEAAHGGNVL ITDTWISMGQ EEEKKKRLQA FQGYQVTMKT AKVAASDWTF 
       310        320        330        340        350    
LHCLPRKPEE VDDEVFYSPR SLVFPEAENR KWTIMAVMVS LLTDYSPQLQ KPKF

Isoforms



Sequence View



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Protein Neighborhood

Domains & Features

2 N-termini - 2 C-termini - 1 Cleavages - 0 Substrates

N-termini

    Name Sequence Position Modification Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMID)
    P00480-25-unknown FRCGQP... 25 inferred from cleavage unknown TopFIND Inferred from cleavage TC26464
    P00480-33-unknown NKVQLK... 33 inferred from electronic annotation electronic annotation UniProtKB inferred from uniprot

C-termini

Cleavages

Substrates

    Substrate Position Sequence Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)