TopFIND 4.0

Q16836: Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial

General Information

Protein names
- Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
- HCDH
- 1.1.1.35
- Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase
- Short-chain 3-hydroxyacyl-CoA dehydrogenase

Gene names HADH
Organism Homo sapiens
Protease Family
Protease ID
Chromosome location
UniProt ID Q16836

14

N-termini

2

C-termini

1

Cleavages

0

Substrates

Sequence

        10         20         30         40         50         60 
MAFVTRQFMR SVSSSSTASA SAKKIIVKHV TVIGGGLMGA GIAQVAAATG HTVVLVDQTE 
        70         80         90        100        110        120 
DILAKSKKGI EESLRKVAKK KFAENLKAGD EFVEKTLSTI ATSTDAASVV HSTDLVVEAI 
       130        140        150        160        170        180 
VENLKVKNEL FKRLDKFAAE HTIFASNTSS LQITSIANAT TRQDRFAGLH FFNPVPVMKL 
       190        200        210        220        230        240 
VEVIKTPMTS QKTFESLVDF SKALGKHPVS CKDTPGFIVN RLLVPYLMEA IRLYERGDAS 
       250        260        270        280        290        300 
KEDIDTAMKL GAGYPMGPFE LLDYVGLDTT KFIVDGWHEM DAENPLHQPS PSLNKLVAEN 
       310    
KFGKKTGEGF YKYK

Isoforms

- Isoform 2 of Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial - Isoform 3 of Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial

Sequence View

        10         20         30         40         50         60 
MAFVTRQFMR SVSSSSTASA SAKKIIVKHV TVIGGGLMGA GIAQVAAATG HTVVLVDQTE 
        70         80         90        100        110        120 
DILAKSKKGI EESLRKVAKK KFAENLKAGD EFVEKTLSTI ATSTDAASVV HSTDLVVEAI 
       130        140        150        160        170        180 
VENLKVKNEL FKRLDKFAAE HTIFASNTSS LQITSIANAT TRQDRFAGLH FFNPVPVMKL 
       190        200        210        220        230        240 
VEVIKTPMTS QKTFESLVDF SKALGKHPVS CKDTPGFIVN RLLVPYLMEA IRLYERGDAS 
       250        260        270        280        290        300 
KEDIDTAMKL GAGYPMGPFE LLDYVGLDTT KFIVDGWHEM DAENPLHQPS PSLNKLVAEN 
       310    
KFGKKTGEGF YKYK         10         20         30         40         50         60 
MAFVTRQFMR SVSSSSTASA SAKKIIVKHV TVIGGGLMGA GIAQVAAATG HTVVLVDQTE 
        70         80         90        100        110        120 
DILAKSKKGI EESLRKVAKK KFAENLKAGD EFVEKTLSTI ATSTDAASVV HSTDLVVEAI 
       130        140        150        160        170        180 
VENLKVKNEL FKRLDKFAAE HTIFASNTSS LQITSIANAT TRQDRFAGLH FFNPVPVMKL 
       190        200        210        220        230        240 
VEVIKTPMTS QKTFESLVDF SKALGKHPVS CKDTPGFIVN RLLVPYLMEA IRLYERGDAS 
       250        260        270        280        290        300 
KEDIDTAMKL GAGYPMGPFE LLDYVGLDTT KFIVDGWHEM DAENPLHQPS PSLNKLVAEN 
       310    
KFGKKTGEGF YKYK



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Protein Neighborhood

Domains & Features

14 N-termini - 2 C-termini - 1 Cleavages - 0 Substrates

N-termini

C-termini

Cleavages

Substrates

    Substrate Position Sequence Evidence type Method Source (database) Source (Lab) Evidence name Publications (PMIDs)